Abstract:Objective: To improve the understanding of total anomalous pulmonary venous connection(TAPVC) and its coexistent malformation. Methods: CT angiography data of 70 patients with TAPVC were retrospectively analyzed, and the coexistent malformation of TAPVC were summarized. Results: Of 70 patients with TAPVC, 42 cases were supracardiac type, 13 cases were cardiac type, 8 cases were infracardiac type, and 7 cases were mixed type. The coexistent malformation of TAPVC can be single or multiple malformation. The coexistent malformation of 70 patients with TAPVC included: atrial septal defect 70 cases(100%), patent ductus arteriosus 31 cases(44.3%), persistent left superior vena cava 5 cases(7.1%), coarctation of aorta and pulmonary valve stenosis 3 cases(4.3%) respectively, pulmonary atresia, single ventricle, dextrocardia, ventricular septal defect and aberrant right subclavian artery 2 cases(2.9%) respectively, endocardial cushions defect, single atrium, unroofed coronary sinus, aortopulmonary window and double outlet right ventricle 1 case(1.4%) respectively. In addition to the patients combined with atrial septal defect and patent ductus arteriosus, only 11 cases(15.7%) combined with other cardiovascular coexistent malformations. Three cases(4.3%) combined with five or more complex coexistent malformations. Conclusion: The morphology and CT findings of TAPVC were complex. The most common coexistent malformations of TAPVC were atrial septal defect and patent ductus arteriosus, which have the tendency of centralized concurrency. Other coexistent malformations were rare, but the types were diversified.
向永华,金 科,徐和平,尹 燕,李春旺. 完全性肺静脉异位引流的CT诊断及合并畸形特点[J]. 中国临床医学影像杂志, 2020, 31(1): 30-33.
XIANG Yong-hua, JIN Ke, XU He-ping, YIN Yan, LI Chun-wang. CT diagnosis of total anomalous pulmonary venous connection and characteristics of coexistent malformation. JOURNAL OF CHINA MEDICAL IMAGING, 2020, 31(1): 30-33.