Abstract：Objective: To evaluate the value of MRI in the patients with atrial isomerism(cardiosplenia syndrome). Methods: Eighty-eight cases with cardiosplenia syndrome(mean age 3.69 years; age range 1 month to 15 years) were evaluated by MRI including FIESTA, double IR and CE-MRA. Results: Right atrial isomerism was seen in 67 cases, all of which were associated with complex congenital heart disease. Bilateral morphologic right bronchi were identified in all of the 67 patients, bilateral superior vena cava in 45 and anomalous pulmonary vein connection in 23. Moreover, anomalous hepatic venous drainage was imaged in 17 and hiatal hernia in 2. Left atrial isomerism was otherwise identified in 21 cases with bilateral morphologic left bronchi. Interruption of inferior vena cava with azygos continuation was present in 16 of 21 cases. Diagnostic accuracy of excardiacvascular anomalies was 100%. Conclusion: MRI can provide accurate diagnosis of complex cardiovascular anomalies as well as status of spleen and bronchus, which is very helpful in diagnosis of complex congential heart disease. The advantages of MRI makes it ideally suited to the evaluation of cardiosplenia syndrome.
2007, Vol. 18 
